FGFR4

Oncogene
Fibroblast growth factor receptor 4 UniProt accession P22455

Tyrosine-protein kinase that acts as a cell-surface receptor for fibroblast growth factors and plays a role in the regulation of cell proliferation, differentiation and migration, and in regulation of lipid metabolism, bile acid biosynthesis, glucose uptake, vitamin D metabolism and phosphate homeostasis. Required for normal down-regulation of the expression of CYP7A1, the rate-limiting enzyme in bile acid synthesis, in response to FGF19. Phosphorylates PLCG1 and FRS2.

Ligand binding leads to the activation of several signaling cascades. Activation of PLCG1 leads to the production of the cellular signaling molecules diacylglycerol and inositol 1,4,5-trisphosphate. Phosphorylation of FRS2 triggers recruitment of GRB2, GAB1, PIK3R1 and SOS1, and mediates activation of RAS, MAPK1/ERK2, MAPK3/ERK1 and the MAP kinase signaling pathway, as well as of the AKT1 signaling pathway.

Promotes SRC-dependent phosphorylation of the matrix protease MMP14 and its lysosomal degradation. FGFR4 signaling is down-regulated by receptor internalization and degradation; MMP14 promotes internalization and degradation of FGFR4. Mutations that lead to constitutive kinase activation or impair normal FGFR4 inactivation lead to aberrant signaling

Source: UniProt

Monomer. Homodimer after ligand binding. Interacts with FGF1, FGF2, FGF4, FGF6, FGF8, FGF9, FGF16, FGF17, FGF18, FGF19, FGF21 and FGF23 (in vitro).

Binding affinity for FGF family members is enhanced by interactions between FGFs and heparan sulfate proteoglycans. Interacts with KLB; this strongly increases the affinity for FGF19 and FGF23. Affinity for FGF19 is strongly increased by KLB and sulfated glycosaminoglycans.

KLB and KL both interact with the core-glycosylated FGFR4 in the endoplasmic reticulum and promote its degradation, so that only FGFR4 with fully mature N-glycans is expressed at the cell surface. Identified in a complex with NCAM1, CDH2, PLCG1, FRS2, SRC, SHC1, GAP43 and CTTN. Interacts with MMP14 and HIP1 (PubMed:11433297, PubMed:16597617, PubMed:17623664, PubMed:18670643, PubMed:20683963, PubMed:20798051, PubMed:21653700, PubMed:7518429, PubMed:8663044).

Interacts with STAT3 (PubMed:26675719)

Source: UniProt
Cell membrane — Single-pass type I membrane protein, Endosome, Endoplasmic reticulum Secreted
Source: UniProt

Expressed in gastrointestinal epithelial cells, pancreas, and gastric and pancreatic cancer cell lines

Source: UniProt
  • Unknown disease
Source: UniProt
  • PI3K Cascade
  • PIP3 activates AKT signaling
  • betaKlotho-mediated ligand binding
  • FGFR4 mutant receptor activation
  • FGFR4 ligand binding and activation
  • Constitutive Signaling by Aberrant PI3K in Cancer
  • Phospholipase C-mediated cascade, FGFR4
  • FRS-mediated FGFR4 signaling
  • SHC-mediated cascade:FGFR4
  • PI-3K cascade:FGFR4
  • Negative regulation of FGFR4 signaling
  • Signaling by FGFR4 in disease
  • RAF/MAP kinase cascade
  • PI5P, PP2A and IER3 Regulate PI3K/AKT Signaling
Source: Reactome via UniProt

Mutations

Cancer Type Mutation Percentage
Central Nervous System Astrocytoma Grade Iv 0.47%
Lung Adenocarcinoma 1.40%
Lung Small Cell Carcinoma 1.48%
Lung Squamous Cell Carcinoma 0.95%
Oesophagus Squamous Cell Carcinoma 0.35%
Pancreas Ductal Carcinoma 0.33%

Synthetic Lethal Network

Genes with an experimentally identified or computationally predicted synthetic-lethal relationship to FGFR4, aggregated across our SSL data sources. Click any partner node to view that gene’s page.

Nodes and edges are coloured by the SSL data source. Partners appearing in more than one source are shown in grey.

BioGRID SLOrth SynLethDB MexDrugs Multi-source
Sources: BioGRID, SLOrth, SynLethDB, MexDrugs

Clinical Trials

Total Trials Found: 12

NCT ID Condition Brief Title Phase Status
NCT06258408 Advanced Solid Tumor A Phase 1 Study of BB102 in Participants With Advanced Solid Tumors PHASE1 RECRUITING
NCT02834780 Advanced Hepatocellular Carcinoma, Hepatocellular Carcinoma, Liver Cancer, Liver Neoplasms, Hepatic Cancer, Hepatic Carcinoma Phase 1 Study to Evaluate the Safety, Pharmacokinetics and Pharmacodynamics of H3B-6527 in Participants With Advanced Hepatocellular Carcinoma PHASE1 COMPLETED
NCT07239986 Hepatocellular Carcinoma (HCC) A Phase 2 Study of BB102 in Patients With Hepatocellular Carcinoma PHASE2 NOT_YET_RECRUITING
NCT06865664 Rhabdomyosarcoma FGFR4 Chimeric Antigen Receptor (CAR) T Cells in Children and Young Adults With Recurrent or Refractory Rhabdomyosarcoma PHASE1 RECRUITING
NCT04699643 Advanced Solid Tumors FGFR4 Inhibitor EVER4010001 in Combination With PD-1 Inhibitor Pembrolizumab in Patients With Advanced Solid Tumors PHASE1, PHASE2 UNKNOWN
NCT05498519 Advanced Solid Tumor A First-in-Human, Phase 1 Study of SY-4798 in Patients With Advanced Solid Tumor PHASE1 UNKNOWN
NCT02325739 Hepatocellular Carcinoma (HCC), Solid Malignancies FGF401 in HCC and Solid Tumors Characterized by Positive FGFR4 and KLB Expression PHASE1, PHASE2 COMPLETED
NCT02508467 Hepatocellular Carcinoma (HCC) A Phase 1 Study of Fisogatinib (BLU-554) in Patients With Hepatocellular Carcinoma PHASE1 COMPLETED
NCT02476019 Obesity A Safety, Tolerability, PK, and PD Study of Once Weekly ISIS-FGFR4RX SC in Obese Patients PHASE2 COMPLETED
NCT01752920 Solid Tumor Phase 1/2 Study of Derazantinib (ARQ 087) in Adult Subjects With Advanced Solid Tumors With FGFR Genetic Alterations PHASE1, PHASE2 COMPLETED